Atresia pulmonar con septum integro pdf

Pulmonary atresia and ventricular septal defect and truncus arteriosus lan nguyen, md duration. Pulmonary atresia with intact interventricular septum. Pulmonary atresia with intact interventricular septum paivs is a subtype of pulmonary atresia that presents as cyanotic congenital heart disease. Pulmonary atresia with intact ventricular septum paivs is a relatively uncommon form of congenital heart disease and is remarkable in its morphologic diversity, characterized by varying degrees of right ventricle rv hypoplasia and associated with tricuspid valve dysplasia and sinusoidal right ventriculocoronary connections. In this form of pulmonary atresia, the wall, or septum, between the ventricles remains complete and intact. Atresia pulmonar con tabique interventricular integro. The valve is completely closed thereby obstructing the outflow of blood from the heart to the lungs. Congenital heart defects facts about pulmonary atresia cdc.

Atresia pulmonar con septum interventricular intacto. Paivs involves complete blockage of the pulmonary valve located on the right side of the heart. Atresia pulmonar con septum interventricular intacto scielo cuba. Pulmonary atresia with intact ventricular septum and critical pulmonary stenosis in newborns encompasses a wide spectrum of disease, including cases with significant right ventricular hypoplasia and coronary artery to right ventricle fistulae, which may be considered a contraindication for decompression of the right ventricle. Pulmonary atresia is a congenital malformation of the pulmonary valve in which the valve orifice fails to develop. Atresia pulmonar con septo integro cirugia cardiovascular. Pathology paivs is the combination of obstruction of the pulmonary outflow tract from pulmona. Caracteristicas morfologicas angiograficas na atresia.

Atresia pulmonar con septum interventricular integro. Pulmonary atresia with intact ventricular septum percutaneous. Atresia pulmonar com septo integroatresia pulmonar com septo integro definicao. Pulmonary atresia with intact ventricular septum paivs is a rare congenital malformation. In patients with pulmonary atresia with intact ventricular septum paivs, radiofrequencyassisted perforation of the valve is the most widely used initial therapy. Atresia pulmonar com comunicacao interventricular cardio. In a normal functioning heart, the opening to the pulmonary valve has. Perforacion y valvuloplastia pulmonar mediante tecnica mecanica modificada. Jun 02, 2011 pulmonary atresia and ventricular septal defect and truncus arteriosus lan nguyen, md duration.

The pulmonary valve is located on the right side of the heart between the right ventricle and pulmonary artery. During pregnancy when the heart is developing, very little blood flows into or out of the right ventricle rv, and therefore the rv doesnt fully develop and remains very small. Atresia pulmonar con septo integro francisco portela, sonia marcos cirugia cardiaca infantil y cardiologia infantil complejo hospitalario juan canalejo. Atresia pulmonar con septo integro asociada a estenosis aortica. Atresia pulmonar con comunicacion interventricular apciv. Pdf pulmonary atresia with intact ventricular septum is an apparently simple cyanotic congenital heart disease. Atresia pulmonar con tabique interventricular integro en una cardiopata congnita ciantica con flujo pulmonar disminuido y cardiomegalia. Atresia pulmonar con septo integro connecting repositories.

Atresia pulmonar con septo integro biventricular 60% fontan 24% uno y medio 12% paliacion 3% trasplante 1% figura 4. Valvulotomia pulmonar percutanea mediante radiofrecuencia en. There is significant morphologic heterogeneity among patients with paivs, 3 and the selection criteria for univentricular or biventricular repair are under debate. Atresia pulmonar con septo integro bive ntricular uno y medio glenn univentricular fontan figura 3.

This blockage prevents the flow of blood to the lungs. A single uniform approach in the management of this disease is. Gonzalez morejon1 ansia serrano sanchez2 giselle serrano ricardo1. Pdf atresia pulmonar con septo integro researchgate. Atresia pulmonar con comunicacion interventricular. Atresia pulmonar con comunicacion interventricular cirugia. Su reparacion requiere multiples operaciones y cateterismos. Pulmonary atresia with an intact ventricular septum. The influence of ventricular morphology and coronary artery dominance and morphology on early mortality in patients with pulmonary atresia and intact ventricular septum. Pulmonary atresia with intact ventricular septum is an. Houston methodist debakey cv education 2,7 views 12.